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Zane F. Pollard, MD; Marc Greenberg, MD; Alice Bashinsky, MD; Mark Bordenca, MD

Arch Ophthalmol. 2007;125(11):1574-1575.

	Since this article does not have an abstract, we have provided the first 150 words of the full text and any section headings.

Typical Cogan syndrome¹ involves nonsyphilitic interstitial keratitis associated with audiovestibular involvement that progresses to complete deafness within 2 years. Atypical Cogan syndrome occurs when sensorineural hearing loss is associated with ocular inflammation distinct from interstitial keratitis, such as uveitis, scleritis, conjunctivitis, or retinal vasculitis. We describe 3 cases of atypical Cogan syndrome that were undiagnosed for a long time. Awareness of this syndrome will aid in the diagnosis and subsequent treatment of this unusual entity. Cogan syndrome is described as typical when it appears in young adults with flare-ups of interstitial keratitis and sudden onset of Ménière disease–like attacks, which progress to sensorineural deafness within 2 years. The keratitis is usually bilateral peripheral subepithelial keratitis, which can progress to nummular lesions. A deep stromal keratitis can occur and vascularization of the cornea usually occurs. Early diagnosis is . . . [Full Text of this Article]

Report of Cases

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